When cor triatriatum is the only abnormality, the clinical findings are also similar to mitral stenosis with development of pulmonary hypertension and subsequent right ventricular hypertrophy and atrial enlargement. Less commonly, the foramen ovale communicates with the distal chamber and the clinical features mimic mitral stenosis.
Most frequently, the upper chamber communicates with the right atrium through a patent foramen ovale or atrial septal defect, and the clinical symptoms simulate anomalous pulmonary venous return. Cor triatriatum is often associated with other congenital cardiac anomalies. The 2 chambers communicate through a defect in the membrane. The upper chamber receives the pulmonary veins and the lower chamber contains the atrial appendage and the mitral valve. Cor triatriatum with complex congenital anomalies may be associated with adverse outcome.Ĭor triatriatum is a rare congenital cardiac anomaly in which the left atrium is divided into proximal (dorsal or upper) and distal (ventral or lower) chambers by a fibromuscular septum. Surgical repair of cor triatriatum provides satisfactory early and long-term survival with low risk for additional intervention. All patients were in New York Heart Association class I or II at a mean follow-up of 12.8 years (maximum 44 years). Kaplan-Meier survival at 10 years was 83%. Two infants who had concomitant repair of complex congenital anomalies died at 2 and 5 months postoperatively after discharge from hospital. None of the patients had any residual atrial obstruction. Twenty patients (80%) required concomitant cardiac surgical procedures. There were 11 males and 14 females with a mean age of 27.4 years (age range, 1 day to 73 years).Īll patients underwent excision of cor triatriatum membrane using cardiopulmonary bypass. Twenty-five patients underwent surgical correction of cor triatriatum between May 1960 and September 2012. We sought to review our surgical experience with cor triatriatum sinister. Cor triatriatum is a rare congenital cardiac defect in which the atrium is divided into 2 chambers by a membrane causing obstruction to the blood flow in either the left atrium (cor triatriatum sinister) or the right atrium (cor triatriatum dexter) eventually leading to cardiac failure.
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